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Abstract
Chronic granulomatous disease (CGD) is a primary immunodeficiency characterized by recurrent infections with certain types of bacteria and fungi. Presented herein is the case of a 29 year old woman with CGD who suffered from bacteria-associated haemophagocytic syndrome and a septic pulmonary embolism following a uterine infection and sepsis, caused by Burkholderia cepacia complex.
- Received:
- Accepted:
- Published Online:
Keyword(s):
ALT, alanine aminotransferase
,
AST, aspartate aminotransferase
,
BAHS, bacteria-associated haemophagocytic syndrome
,
BCC, Burkholderia cepacia complex
,
CGD, chronic granulomatous disease
,
CRP, C-reactive protein
,
CSA, cyclosporin A
,
CT, computed tomography
,
HPS, haemophagocytic syndrome
,
IL, interleukin
,
LDH, lactate dehydrogenase
,
PSL, prednisolone
,
TNF-α, tumour necrosis factor alpha
and
WBC, white blood cells
SGM